Successful Management of Pregnancy in Uncorrected Tetralogy of Fallot with Pulmonary Atresia.

Tetralogy of Fallot (TOF) is the commonest congenital cyanotic heart disorder, accounting for 5–6 % of them [1]. It is characterized by a large ventricular septal defect, right ventricular outflow tract obstruction, right ventricular hypertrophy, and aorta overriding the interventricular septum. Most patients with TOF undergo reparative surgery in childhood. TOF with pulmonary atresia is the extreme end of anatomic spectrum which is difficult to correct surgically. Pregnancy in uncorrected TOF entails serious risks including increased maternal morbidity, mortality up to 15 %, and poor perinatal outcome [2]. We report a case of pregnancy in uncorrected TOF with pulmonary atresia which was successfully managed at a tertiary care center with multidisciplinary approach.